- premature death / MGI
- increased susceptibility to infection / MGI
- absent lymph nodes / MGI
- decreased mast cell number / MGI
- abnormal intestinal epithelium morphology / MGI
- abnormal salivary gland morphology / MGI
- abnormal mammary gland development / MGI
- abnormal immune system morphology / MGI
- small thymus / MGI
- abnormal immune system physiology / MGI
- abnormal T cell activation / MGI
- increased inflammatory response / MGI
- kidney inflammation / MGI
- liver inflammation / MGI
- lung inflammation / MGI
- pancreas inflammation / MGI
- abnormal hepatobiliary system morphology / MGI
- abnormal thymus medulla morphology / MGI
- abnormal dendritic cell physiology / MGI
- abnormal dendritic cell antigen presentation / MGI
- decreased IgE level / MGI
- absent Peyer's patches / MGI
- abnormal bile duct morphology / MGI
- dilated bile duct / MGI
- bile duct inflammation / MGI
- bile duct proliferation / MGI
- abnormal intestinal goblet cell morphology / MGI
- bile duct hyperplasia / MGI
- decreased regulatory T cell number / MGI
- increased eosinophil cell number / MGI
- increased susceptibility to parasitic infection / MGI
- abnormal NK T cell morphology / MGI
- decreased NK T cell number / MGI
- decreased dendritic cell number / MGI
- abnormal CD4-positive, CD25-positive, alpha-beta regulatory T cell morphology / MGI
- decreased circulating interferon-gamma level / MGI
- decreased circulating interleukin-4 level / MGI
- lacrimal gland inflammation / MGI
- abnormal mammary fat pad morphology / MGI
- decreased mammary fat pad weight / MGI
- abnormal thymus corticomedullary boundary morphology / MGI
- thymus cysts / MGI
- decreased IgG level / MGI
- decreased IgM level / MGI
- decreased IgA level / MGI
- abnormal lymphopoiesis / MGI
- abnormal lymphocyte morphology / MGI
- increased length of allograft survival / MGI
- decreased B cell number / MGI
- absent follicular dendritic cells / MGI
- absent spleen marginal zone / MGI
- abnormal spleen B cell follicle morphology / MGI
- abnormal spleen primary B follicle morphology / MGI
- mortality/aging / MGI
- absent thymus corticomedullary boundary / MGI
B6(Cg)-Map3k14aly/Ieg
Status | Available to order |
EMMA ID | EM:07800 |
International strain name | B6(Cg)-Map3k14aly/Ieg |
Alternative name | C57BL/6J-Map3k14 |
Strain type | Spontaneous |
Allele/Transgene symbol | Map3k14aly |
Gene/Transgene symbol | Map3k14 |
Information from provider
Provider | Joerg Kirberg |
Provider affiliation | Div. of Immunology (3/3), Paul-Ehrlich-Institut |
Genetic information | Mice carry the known mutation of Map3k14 (mitogen-activated protein kinase kinase kinase 14, aka NIK, NF-kB inducing kinase) termed aly (alymphoplasia). That mutation arose spontaneously on a mixed background (AEJ/GnRk * C57BL/6J; The Jackson Lab ref. J:16865, PubMed ref. PMID 8299692) and was later identified as G-to-A transition point mutation resulting in a replacement of a conserved glycine for an arginine at position 855 of the encoded protein (The Jackson Lab ref. J:54529; PubMed ref. PMID 10319865). The mutant allele was reported to be bred to C57BL/6. However, variations in the proportions of marginal B cells in the spleen, reported to be absent in aly mice, were observed here. For this reason, the mutant allele was backcrossed to C57BL/6 for 12 generations (exchanging the sex chromosomes along). |
Phenotypic information | Homozygous:Alymphoplasia, see The Jackson Lab ref. J:16865, PubMed ref. PMID 8299692. Underlying mutation: see The Jackson Lab ref. J:54529, PubMed ref. PMID 10319865.Heterozygous:nothing obvious |
Breeding history | The mutant allele was backcrossed to C57BL/6 for 12 generations (exchanging the sex chromosomes along). Following this, the line was expanded by intercrossing to obtain aly/aly homozygotes. Since aly/aly females are supposedly unable to lactate, the line is maintained as aly heterozygous females mated with aly/aly homozygous males. |
References |
|
Homozygous fertile | males only |
Homozygous viable | yes |
Homozygous matings required | no |
Immunocompromised | yes |
Information from EMMA
Archiving centre | Helmholtz Zentrum Muenchen - German Research Center for Environmental Health (GmbH), Oberschleißheim, Germany |
Animals used for archiving | heterozygous C57BL/6J, wild-type C57BL/6J |
Stage of embryos | 2-cell |
Disease and phenotype information
MGI allele-associated human disease models
Orphanet associated rare diseases, based on orthologous gene matching
- NIK deficiency / Orphanet_447731
MGI phenotypes (allele matching)
MGI phenotypes (gene matching)
- decreased mast cell number / MGI
- abnormal intestinal epithelium morphology / MGI
- abnormal salivary gland morphology / MGI
- abnormal mammary gland development / MGI
- abnormal immune system morphology / MGI
- abnormal spleen morphology / MGI
- abnormal thymus morphology / MGI
- small thymus / MGI
- abnormal immune system physiology / MGI
- arrested B cell differentiation / MGI
- decreased IgG level / MGI
- decreased IgM level / MGI
- decreased IgA level / MGI
- abnormal T cell activation / MGI
- increased inflammatory response / MGI
- kidney inflammation / MGI
- liver inflammation / MGI
- lung inflammation / MGI
- pancreas inflammation / MGI
- premature death / MGI
- abnormal hepatobiliary system morphology / MGI
- abnormal spleen marginal zone morphology / MGI
- abnormal thymus medulla morphology / MGI
- abnormal dendritic cell physiology / MGI
- abnormal lymphopoiesis / MGI
- increased susceptibility to infection / MGI
- abnormal dendritic cell antigen presentation / MGI
- abnormal B cell physiology / MGI
- decreased immunoglobulin level / MGI
- decreased IgE level / MGI
- abnormal lymphocyte morphology / MGI
- absent Peyer's patches / MGI
- abnormal bile duct morphology / MGI
- dilated bile duct / MGI
- bile duct inflammation / MGI
- bile duct proliferation / MGI
- abnormal intestinal goblet cell morphology / MGI
- increased length of allograft survival / MGI
- abnormal class switch recombination / MGI
- bile duct hyperplasia / MGI
- decreased regulatory T cell number / MGI
- increased eosinophil cell number / MGI
- decreased B cell number / MGI
- increased susceptibility to parasitic infection / MGI
- absent lymph nodes / MGI
- abnormal NK T cell morphology / MGI
- decreased NK T cell number / MGI
- decreased dendritic cell number / MGI
- decreased follicular B cell number / MGI
- decreased germinal center B cell number / MGI
- decreased marginal zone B cell number / MGI
- absent follicular dendritic cells / MGI
- decreased B-2 B cell number / MGI
- abnormal B cell activation / MGI
- absent spleen marginal zone / MGI
- abnormal CD4-positive, CD25-positive, alpha-beta regulatory T cell morphology / MGI
- absent mesenteric lymph nodes / MGI
- abnormal spleen B cell follicle morphology / MGI
- abnormal spleen primary B follicle morphology / MGI
- decreased IgG2b level / MGI
- decreased circulating interferon-gamma level / MGI
- decreased circulating interleukin-4 level / MGI
- abnormal thymus cell ratio / MGI
- lacrimal gland inflammation / MGI
- abnormal mammary fat pad morphology / MGI
- decreased mammary fat pad weight / MGI
- abnormal thymus corticomedullary boundary morphology / MGI
- absent inguinal lymph nodes / MGI
- small brachial lymph nodes / MGI
- absent axillary lymph nodes / MGI
- small axillary lymph nodes / MGI
- absent cervical lymph nodes / MGI
- absent popliteal lymph nodes / MGI
- decreased transitional stage T1 B cell number / MGI
- decreased transitional stage T2 B cell number / MGI
- mortality/aging / MGI
- absent thymus corticomedullary boundary / MGI
- thymus cysts / MGI
Literature references
- A new mutation, aly, that induces a generalized lack of lymph nodes accompanied by immunodeficiency in mice.;Miyawaki S, Nakamura Y, Suzuka H, Koba M, Yasumizu R, Ikehara S, Shibata Y, ;1994;European journal of immunology;24;429-34; 8299692
- Alymphoplasia is caused by a point mutation in the mouse gene encoding Nf-kappa b-inducing kinase.;Shinkura R, Kitada K, Matsuda F, Tashiro K, Ikuta K, Suzuki M, Kogishi K, Serikawa T, Honjo T, ;1999;Nature genetics;22;74-7; 10319865
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