- decreased rhombomere 3 size / MGI
STOCK Egr2tm3Pch Egr3tm1Jmi Tg(CD2-icre)4Kio Tg(Tbx21-AmCyan)Jfz/H
Status | Only small colony available |
EMMA ID | EM:15287 |
International strain name | STOCK Egr2tm3Pch Egr3tm1Jmi Tg(CD2-icre)4Kio Tg(Tbx21-AmCyan)Jfz/H |
Alternative name | AmCyanTbet-Egr3/2 double Knockout |
Strain type | Transgenic Strains |
Allele/Transgene symbol | Tg(CD2-icre)4Kio, Egr2tm3Pch, Egr3tm1Jmi |
Gene/Transgene symbol | Tg(CD2-icre)4Kio, Egr2, Egr3, Tg-AmCyanTbet |
Information from provider
Provider | Suling Li |
Provider affiliation | Brunel University |
Genetic information | AmCyan-T-bet reporter mouse line (Yu et al., Nat. Immunol., 2015) crossed with a Egr3-/- and CD2-specific Egr2-/-(CD2-Egr2-/-;Egr3-/-) mice line, which was generated by interbreeding Egr3 KO (Tourtellotte and Milbrandt, Nat Genet 1998; MGI:2180063, symbol Egr3tm1Jmi) and CD2-specific Egr2 KO mice (Zhu et al., J Exp Med 2008; Li et al., Immunity 2012; Egr2-flox: MGI:2183227, symbol Egr2tm3Pch; CD2-Cre: MGI:2449947, symbol Tg(CD2-icre)4Kio). More than 30 backcrosses. |
Phenotypic information | Homozygous:The knock-out mice with deletion of both transcription factors Egr2 and Egr3 in lymphocytes resulted in a lethal autoimmune syndrome with excessive serum proinflammatory cytokines but also impaired antigen receptor-induced proliferation of B and T cells.Heterozygous:Inflammation similar as homozygous but less severe. |
Breeding history | The AmCyan-T-bet reporter mouse line (Yu et al., 2015) was crossed with a Egr3-/- and CD2-specific Egr2-/- (CD2-Egr2-/-Egr3-/-) mice line, which was generated by interbreeding Egr3 knock-out (Tourtellotte and Milbrandt, 1998) and CD2-specific Egr2 knock-out mice (Zhu et al., J Exp Med 2008; Li et al., Immunity 2012). More than 30 backcrosses. |
References | None available |
Homozygous fertile | yes |
Homozygous viable | yes |
Homozygous matings required | no |
Immunocompromised | no |
Information from EMMA
Archiving centre | Mary Lyon Centre at MRC Harwell, Oxford, United Kingdom |
Disease and phenotype information
Orphanet associated rare diseases, based on orthologous gene matching
- Dejerine-Sottas syndrome / Orphanet_64748
- Charcot-Marie-Tooth disease type 1D / Orphanet_101084
- Charcot-Marie-Tooth disease type 4E / Orphanet_99951
MGI phenotypes (allele matching)
MGI phenotypes (gene matching)
- abnormal mandible morphology / MGI
- tremors / MGI
- weakness / MGI
- paralysis / MGI
- hindlimb paralysis / MGI
- abnormal myelination / MGI
- abnormal rhombomere morphology / MGI
- abnormal motor neuron morphology / MGI
- abnormal spinal cord morphology / MGI
- abnormal neuromuscular synapse morphology / MGI
- abnormal cranial nerve morphology / MGI
- abnormal trigeminal nerve morphology / MGI
- abnormal abducens nerve morphology / MGI
- abnormal facial nerve morphology / MGI
- abnormal glossopharyngeal nerve morphology / MGI
- abnormal vagus nerve morphology / MGI
- abnormal cranial ganglia morphology / MGI
- abnormal geniculate ganglion morphology / MGI
- abnormal trigeminal ganglion morphology / MGI
- abnormal glossopharyngeal ganglion morphology / MGI
- abnormal vagus ganglion morphology / MGI
- abnormal Schwann cell morphology / MGI
- decreased body weight / MGI
- weight loss / MGI
- decreased body size / MGI
- delayed eyelid opening / MGI
- hypoactivity / MGI
- impaired coordination / MGI
- abnormal gait / MGI
- impaired limb coordination / MGI
- postnatal growth retardation / MGI
- respiratory distress / MGI
- abnormal motor capabilities/coordination/movement / MGI
- abnormal skeleton development / MGI
- abnormal neural tube morphology / MGI
- abnormal sciatic nerve morphology / MGI
- abnormal aortic valve morphology / MGI
- abnormal somatic nervous system morphology / MGI
- short tibia / MGI
- abnormal cochlear ganglion morphology / MGI
- abnormal bone mineralization / MGI
- no phenotypic analysis / MGI
- abnormal long bone epiphyseal plate morphology / MGI
- short femur / MGI
- decreased width of hypertrophic chondrocyte zone / MGI
- abnormal long bone morphology / MGI
- abnormal bone structure / MGI
- short radius / MGI
- fusion of glossopharyngeal and vagus nerve / MGI
- decreased length of long bones / MGI
- increased pulmonary respiratory rate / MGI
- abnormal neuronal migration / MGI
- abnormal hindbrain development / MGI
- decreased diameter of long bones / MGI
- decreased diameter of femur / MGI
- decreased diameter of radius / MGI
- decreased diameter of tibia / MGI
- decreased nerve conduction velocity / MGI
- enlarged aortic valve / MGI
- thick aortic valve cusps / MGI
- thick pulmonary valve cusps / MGI
- integument phenotype / MGI
- lethality at weaning, complete penetrance / MGI
- postnatal lethality, complete penetrance / MGI
- postnatal lethality, incomplete penetrance / MGI
- neonatal lethality, incomplete penetrance / MGI
- increased Schwann cell proliferation / MGI
- decreased rhombomere 3 size / MGI
- absent rhombomere 3 / MGI
- decreased rhombomere 5 size / MGI
- absent rhombomere 5 / MGI
- decreased rhombomere 6 size / MGI
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